I think that is correct, but I also don't think it means that it won't work on R334W. R117H is both a conductance and a gating mutation, and Kalydeco helps correct the problem with channel gating. I'm not sure if R334W is just a conductance mutation or if it also has reduced channel gatiing. But, even if it just a conductance mutation, Kalydeco still may help because there is some CFTR present on the cell surface.
When you take a deep breath and blow hard to fully empty your lungs completely into what is loosely referred to as a spirometer, the Forced expressed (air) volume Fev is meaasured. I can only guess the 1 is a simple test. A similar test except you are sealed in a chamber measures your Fev1 and measures your body volume displacement increase as you inhale and exhale. Maybe this spirometer/volumeter has a different number associated with it like maybe FEV2?