Anyone take this? (Long-term inhaled dry powder mannitol improves lung function in CF

rmotion

New member
[h=1]Anyone take mannitol treatments? Long-term inhaled dry powder mannitol improves lung function in CF[/h][h=2][/h]Adding inhaled dry powder mannitol to standard therapy for cystic fibrosis produced sustained improvement in lung function for up to 52 weeks, according to a new study. Along with the treatment's efficacy and good safety profile, the convenience and ease of administration of mannitol treatment may improve adherence with therapy in these patients.
In the double-blind study, which was supported by Pharmaxis Limited, 318 patients were randomized to treatment with 400 mg bid inhaled mannitol or 50 mg bid inhaled mannitol (control group) for 26 weeks, followed by an additional 26 weeks of open-label active treatment. A 50 mg dose was chosen as the control because it was felt it would not be clinically effective, based on an earlier dose escalation study. Mannitol was given on top of a background of typical concomitant therapy such as recombinant human deoxyribonuclease and inhaled antibiotics.
The findings were published online ahead of print publication in the American Thoracic Society's American Journal of Respiratory and Critical Care Medicine.
"Patients in the treatment group showed a 106.5 mL mean improvement in forced expiratory volume in one second (FEV1), an 8.22 percent improvement from baseline, compared with a 52.4 mL improvement (4.47 percent) in the control group," said lead author Moira L. Aitken, MD, professor of pulmonary and critical care medicine at the University of Washington Medical Center. "Forced vital capacity increased 136.3 mL in the treatment group, compared with 65.0 mL in the control group. Treated patients also experienced fewer pulmonary exacerbations than controls."
The difference in absolute FEV1 between the study and control groups approached statistical significance (p=0.059), while the difference in relative change from baseline FEV1 between groups reached significance (p=0.029). Improvements in FEV1 were maintained in the treatment group during the 26-week open-label extension phase of the study. In the control group, mean FEV1 improved 84.0 mL (6.3 percent) from baseline during the open-label phase.
Patients in the treatment and control groups experienced similar rates of adverse events. Given a possible influence of mannitol on lung microbiology, qualitative sputum microbiology was performed for Staphylococcus aureus and Pseudomonas aeruginosa during the double-blind study period. No qualitative changes in microbiology results from baseline were observed in either group.
Compliance was good in both groups, with 85.2 percent of patients in the treatment group and 88.7 percent of controls using 60 percent or more of the drug dispensed.
Although the primary end point for the study, the difference in absolute FEV1 between the treatment and control groups, did not reach significance, this may have been due to use of a single baseline visit to establish baseline FEV1 values. When baseline FEV1 values were calculated as an average of FEV1 values over two baseline visits, as in prior clinical intervention studies, the overall increase in absolute FEV1 was significantly (p=0.0008) greater in the treatment group. The 50 mg dose of mannitol used in the control group may also have had some benefit, which limited the absolute difference between groups.
"In our patients with cystic fibrosis, treatment with inhaled mannitol resulted in sustained improvements in lung function over 12 months, with a favorable safety profile," concluded Dr. Aitken. "In addition, the dry-powder inhaler used to administer mannitol is small, portable, easy to use and doesn't require thorough cleaning and disinfection after each use, which may help patients better adhere to treatment. Our results support the use of inhaled mannitol for the daily management of cystic fibrosis."
 

triples15

Super Moderator
I was in the study. However, after reading this, I'm unsure if I was in THIS study, or the earlier one with the lower dosage. It was prob 3-4 years ago or so. At first I found the capsules really hard to inhale, but I got used to it. The first puff always caused coughing, but after that it was pretty much smooth sailing. I had one exacerbation during the study, but still ended up with a 2% increase in my FEV1 by the end. I feel like it did help me.

It's not approved here (US) but I think it did get approved in Europe if memory serves. So maybe someone who takes it will see this and let us know!

Autumn 32 w/CF
 

occupyjapan

New member
The FDA nixed this in America, unfortunately. Pharmaxis was trying to say it was safe for younger children but didn't have the research to back it up (a lot of kids dropped out of the trial because, yeah, it does cause coughing and stuff and you know how kids are even with treatment that feels good-to-neutral). The company tried revising their age range but the FDA was like "not without another trial, you don't" and as far as I know, the drug is currently in limbo and Pharmaxis, as far as I know, doesn't have any plans to do another trial. They may have just said "screw it" and given up on America, since it's approved pretty much everywhere else in the world already. Clinical trials are expensive and lengthy and it may just not have been in their financial best interests. A shame, since I was really looking forward to trying it.
 
Top