CF? Or NOT? Help.

mandapanda323

New member
I am currently awaiting the results of my 17 month-old's sweat test, but I had some questions and concerns that I'm interested to hear feedback on while I wait.

To give a little background, I started worrying about my child having CF when she was considered "failure to thrive." Our pediatrician did not voice major concern about this, but when my baby had not even doubled her birth weight at 7 months, I became overly concerned. We went on repeated checkups and visits, all in which ended up being a huge waste of time. She remained in the 2nd percentile for several months, but I was told that as long as she was growing proportionally with the chart that there was no need for alarm. I felt like I was being stonewalled for feeling concerned. At 7 months she BARELY weighed 10 lbs, even though she was eating all the time it seemed. After trying to placate me, our pediatrician ordered a spot sweat test which came back negative. I began research on what could possibly be the cause of her low weight, and was constantly directed to CF. Of course, I read all of the other symptoms, as well, and all "could have" fit, but I wasn't quite sure. I don't know that she was "overly" salty when she would sweat. Yes, she was salty when she would sweat, but not necessarily any more than any other sweaty baby. As far as poops, I can only think to compare them with those of my other children- hers have always been what I would call "teething poops." VERY smelly, but not necessarily greasy, and very loose. I honestly can't remember her ever having a solid bowel movement. They are still this way, but once again, can it be chalked up to the fact that maybe she actually IS teething?

After the sweat test was negative, I vowed to put the possibility of CF off of the table. We were CONSTANTLY sick with respiratory infections- RSV at 3 weeks (hospital stay but no oxygen), pneumonia about 5 times, followed by another bout of RSV (in the dead of summer), followed by MORE pneumonia, and FINALLY a third bout of RSV that required hospitalization and almost a week of oxygen. Between all of these major illnesses, we have also had ear infection after ear infection- to where we finally put tubes, only to be followed by the same amount of ear infections as if she didn't have tubes at all. Once again our pediatrician showed little true worry, and always took excellent care of her when she was very ill. Every time I voiced my concern about her chest being "rattley", he would tell me that it sometimes takes a very young baby up to a year to get back to "normal" breathing after having severe RSV. During the last round of RSV, I insisted that we see a Pulmonologist.

Upon meeting with the Pulmonologist, he listed 10 possiblities- asthma, allergies, small airways, etc... CF was on the list, but he explained it was a very low possibility due to the Louisiana newborn screen test. He also looked at her previous x-rays, and agreed that she had been sick in an overabundance, and decided to perform a bronchoscopy and CT scan to get a closer look at her lungs and airways. We had the surgery yesterday, and I was completely taken aback by his findings. Her lungs were filled with thick glue-like mucus in the lower lobes. He showed us the pictures and gave very detailed descriptions of what the mucus was like- and immediately voiced his concerns that it was, in fact, CF. He had us have an electrode sweat test, which leaves us where we are now. Waiting until Friday for the results due to when the lab operates at the hospital where the procedure was performed.

I am now on a complete roller-coaster since I was told SEVERAL times that the odds of her having this disease were low. But now he's all of a sudden concerned? She has never suffered from any pancreatic disorders that I know of, but tons and tons of respiratory infections. Her ears are constantly leaking a thick, glue like substance that has recently developed a pungent odor. I bring her to the ENT, we put her on antibiotics and it's like they do NOTHING. He finally quit putting her on them and she just takes drops to keep the tubes from clogging. She has put on some weight (18 lbs at 17 months), but in general she looks healthy. She is very short and even has some pudge on her. But her belly is swollen, which I later read is also a symptom of CF. Because I was so shocked with the concerns of the Pulmonologist, I have questions I forgot to ask. If the CF test comes back negative- what else could be causing the mucus on the lungs? Are there other diseases that this happens in?
 

mandapanda323

New member
I am currently awaiting the results of my 17 month-old's sweat test, but I had some questions and concerns that I'm interested to hear feedback on while I wait.

To give a little background, I started worrying about my child having CF when she was considered "failure to thrive." Our pediatrician did not voice major concern about this, but when my baby had not even doubled her birth weight at 7 months, I became overly concerned. We went on repeated checkups and visits, all in which ended up being a huge waste of time. She remained in the 2nd percentile for several months, but I was told that as long as she was growing proportionally with the chart that there was no need for alarm. I felt like I was being stonewalled for feeling concerned. At 7 months she BARELY weighed 10 lbs, even though she was eating all the time it seemed. After trying to placate me, our pediatrician ordered a spot sweat test which came back negative. I began research on what could possibly be the cause of her low weight, and was constantly directed to CF. Of course, I read all of the other symptoms, as well, and all "could have" fit, but I wasn't quite sure. I don't know that she was "overly" salty when she would sweat. Yes, she was salty when she would sweat, but not necessarily any more than any other sweaty baby. As far as poops, I can only think to compare them with those of my other children- hers have always been what I would call "teething poops." VERY smelly, but not necessarily greasy, and very loose. I honestly can't remember her ever having a solid bowel movement. They are still this way, but once again, can it be chalked up to the fact that maybe she actually IS teething?

After the sweat test was negative, I vowed to put the possibility of CF off of the table. We were CONSTANTLY sick with respiratory infections- RSV at 3 weeks (hospital stay but no oxygen), pneumonia about 5 times, followed by another bout of RSV (in the dead of summer), followed by MORE pneumonia, and FINALLY a third bout of RSV that required hospitalization and almost a week of oxygen. Between all of these major illnesses, we have also had ear infection after ear infection- to where we finally put tubes, only to be followed by the same amount of ear infections as if she didn't have tubes at all. Once again our pediatrician showed little true worry, and always took excellent care of her when she was very ill. Every time I voiced my concern about her chest being "rattley", he would tell me that it sometimes takes a very young baby up to a year to get back to "normal" breathing after having severe RSV. During the last round of RSV, I insisted that we see a Pulmonologist.

Upon meeting with the Pulmonologist, he listed 10 possiblities- asthma, allergies, small airways, etc... CF was on the list, but he explained it was a very low possibility due to the Louisiana newborn screen test. He also looked at her previous x-rays, and agreed that she had been sick in an overabundance, and decided to perform a bronchoscopy and CT scan to get a closer look at her lungs and airways. We had the surgery yesterday, and I was completely taken aback by his findings. Her lungs were filled with thick glue-like mucus in the lower lobes. He showed us the pictures and gave very detailed descriptions of what the mucus was like- and immediately voiced his concerns that it was, in fact, CF. He had us have an electrode sweat test, which leaves us where we are now. Waiting until Friday for the results due to when the lab operates at the hospital where the procedure was performed.

I am now on a complete roller-coaster since I was told SEVERAL times that the odds of her having this disease were low. But now he's all of a sudden concerned? She has never suffered from any pancreatic disorders that I know of, but tons and tons of respiratory infections. Her ears are constantly leaking a thick, glue like substance that has recently developed a pungent odor. I bring her to the ENT, we put her on antibiotics and it's like they do NOTHING. He finally quit putting her on them and she just takes drops to keep the tubes from clogging. She has put on some weight (18 lbs at 17 months), but in general she looks healthy. She is very short and even has some pudge on her. But her belly is swollen, which I later read is also a symptom of CF. Because I was so shocked with the concerns of the Pulmonologist, I have questions I forgot to ask. If the CF test comes back negative- what else could be causing the mucus on the lungs? Are there other diseases that this happens in?
 

mandapanda323

New member
I am currently awaiting the results of my 17 month-old's sweat test, but I had some questions and concerns that I'm interested to hear feedback on while I wait.
<br />
<br />To give a little background, I started worrying about my child having CF when she was considered "failure to thrive." Our pediatrician did not voice major concern about this, but when my baby had not even doubled her birth weight at 7 months, I became overly concerned. We went on repeated checkups and visits, all in which ended up being a huge waste of time. She remained in the 2nd percentile for several months, but I was told that as long as she was growing proportionally with the chart that there was no need for alarm. I felt like I was being stonewalled for feeling concerned. At 7 months she BARELY weighed 10 lbs, even though she was eating all the time it seemed. After trying to placate me, our pediatrician ordered a spot sweat test which came back negative. I began research on what could possibly be the cause of her low weight, and was constantly directed to CF. Of course, I read all of the other symptoms, as well, and all "could have" fit, but I wasn't quite sure. I don't know that she was "overly" salty when she would sweat. Yes, she was salty when she would sweat, but not necessarily any more than any other sweaty baby. As far as poops, I can only think to compare them with those of my other children- hers have always been what I would call "teething poops." VERY smelly, but not necessarily greasy, and very loose. I honestly can't remember her ever having a solid bowel movement. They are still this way, but once again, can it be chalked up to the fact that maybe she actually IS teething?
<br />
<br />After the sweat test was negative, I vowed to put the possibility of CF off of the table. We were CONSTANTLY sick with respiratory infections- RSV at 3 weeks (hospital stay but no oxygen), pneumonia about 5 times, followed by another bout of RSV (in the dead of summer), followed by MORE pneumonia, and FINALLY a third bout of RSV that required hospitalization and almost a week of oxygen. Between all of these major illnesses, we have also had ear infection after ear infection- to where we finally put tubes, only to be followed by the same amount of ear infections as if she didn't have tubes at all. Once again our pediatrician showed little true worry, and always took excellent care of her when she was very ill. Every time I voiced my concern about her chest being "rattley", he would tell me that it sometimes takes a very young baby up to a year to get back to "normal" breathing after having severe RSV. During the last round of RSV, I insisted that we see a Pulmonologist.
<br />
<br />Upon meeting with the Pulmonologist, he listed 10 possiblities- asthma, allergies, small airways, etc... CF was on the list, but he explained it was a very low possibility due to the Louisiana newborn screen test. He also looked at her previous x-rays, and agreed that she had been sick in an overabundance, and decided to perform a bronchoscopy and CT scan to get a closer look at her lungs and airways. We had the surgery yesterday, and I was completely taken aback by his findings. Her lungs were filled with thick glue-like mucus in the lower lobes. He showed us the pictures and gave very detailed descriptions of what the mucus was like- and immediately voiced his concerns that it was, in fact, CF. He had us have an electrode sweat test, which leaves us where we are now. Waiting until Friday for the results due to when the lab operates at the hospital where the procedure was performed.
<br />
<br />I am now on a complete roller-coaster since I was told SEVERAL times that the odds of her having this disease were low. But now he's all of a sudden concerned? She has never suffered from any pancreatic disorders that I know of, but tons and tons of respiratory infections. Her ears are constantly leaking a thick, glue like substance that has recently developed a pungent odor. I bring her to the ENT, we put her on antibiotics and it's like they do NOTHING. He finally quit putting her on them and she just takes drops to keep the tubes from clogging. She has put on some weight (18 lbs at 17 months), but in general she looks healthy. She is very short and even has some pudge on her. But her belly is swollen, which I later read is also a symptom of CF. Because I was so shocked with the concerns of the Pulmonologist, I have questions I forgot to ask. If the CF test comes back negative- what else could be causing the mucus on the lungs? Are there other diseases that this happens in?
 
S

sdelorenzo

Guest
I can imagine you are anxious about the results. Was the sweat test done at an accredited CF Center? Go to:
<a target=_blank class=ftalternatingbarlinklarge href="http://www.cff.org/LivingWithCF/CareCenterNetwork/CFFoundation-accreditedCareCenters/
">http://www.cff.org/LivingWithC...ccreditedCareCenters/
</a>It is important to have sweat tests done only at these centers because local hospitals can perform the test inaccurately. It is common to get the results back in 2 or 3 hours, not 3 days. Yes, your daughter does have some symptoms of CF. But the fact that she passed the newborn screening is good news. If the CF test comes back negative you need to tell the pulmonologist that you want your child to have the Ambry genetic test. Just because a child passes a sweat test does not mean they can't have CF. Also be sure to ask what the score of her sweat test is. Below 30 negative and 30-59 borderline. Hope you get some answers soon.
Sharon, mom of Sophia, 9 and Jack, 7 both with cf, Grant, 2 and Paige, 6 months both without cf
 
S

sdelorenzo

Guest
I can imagine you are anxious about the results. Was the sweat test done at an accredited CF Center? Go to:
<a target=_blank class=ftalternatingbarlinklarge href="http://www.cff.org/LivingWithCF/CareCenterNetwork/CFFoundation-accreditedCareCenters/
">http://www.cff.org/LivingWithC...ccreditedCareCenters/
</a>It is important to have sweat tests done only at these centers because local hospitals can perform the test inaccurately. It is common to get the results back in 2 or 3 hours, not 3 days. Yes, your daughter does have some symptoms of CF. But the fact that she passed the newborn screening is good news. If the CF test comes back negative you need to tell the pulmonologist that you want your child to have the Ambry genetic test. Just because a child passes a sweat test does not mean they can't have CF. Also be sure to ask what the score of her sweat test is. Below 30 negative and 30-59 borderline. Hope you get some answers soon.
Sharon, mom of Sophia, 9 and Jack, 7 both with cf, Grant, 2 and Paige, 6 months both without cf
 
S

sdelorenzo

Guest
I can imagine you are anxious about the results. Was the sweat test done at an accredited CF Center? Go to:
<br /><a target=_blank class=ftalternatingbarlinklarge href="http://www.cff.org/LivingWithCF/CareCenterNetwork/CFFoundation-accreditedCareCenters/
">http://www.cff.org/LivingWithC...ccreditedCareCenters/
</a><br />It is important to have sweat tests done only at these centers because local hospitals can perform the test inaccurately. It is common to get the results back in 2 or 3 hours, not 3 days. Yes, your daughter does have some symptoms of CF. But the fact that she passed the newborn screening is good news. If the CF test comes back negative you need to tell the pulmonologist that you want your child to have the Ambry genetic test. Just because a child passes a sweat test does not mean they can't have CF. Also be sure to ask what the score of her sweat test is. Below 30 negative and 30-59 borderline. Hope you get some answers soon.
<br />Sharon, mom of Sophia, 9 and Jack, 7 both with cf, Grant, 2 and Paige, 6 months both without cf
 

mom2owen

New member
Hi, Welcome! I am sorry you are here but I am sure you will get some great ideas from the other members. It is a really hard thing to wait out such a serious possibility. It sounds like you are getting very good care so far and that is really half the battle. It is hard to say what is or is not CF from the descriptions we all have of our kids. Mine is one of those really tough cases who shows many symptoms, but lab tests are not adding up. That said, we deal with g-tube feedings for failure to thrive, he is on enzymes, he does CPT and is on nebs and antibiotics for infections often, much like your story. So, my two cents is that even when it could be something else or isn't clear cut, the most important thing I have learned in our 7 year struggle is that the care you receive is the most important thing. Lots of people are misdiagnosed with asthma which can also cause a lot of mucus build up. There could potentially be other things that are causing your daughters difficulties but the treatments are also often the same so I am glad you are getting help and people taking you seriously. I think when we as mothers know something is wrong, doctors need to listen!
I know others will offer a lot more help than I can but I wanted to share my welcome and thoughts. I sure hope you find out something good and helpful soon. Are you also having genetics testing done? Perhaps after the sweat test? No test is 100% but it sure helps to know you have done all you can to figure it out. For us, CF is the one disease that has come up over and over again from all the doctors we have gone to. It hasn't gotten any easier in terms of knowing something concrete, but it has brought our level of treatment up and that is the best I can hope for with my own son for now.
Hang in there, I know how hard this is. Take care and let me know what you find out.
 

mom2owen

New member
Hi, Welcome! I am sorry you are here but I am sure you will get some great ideas from the other members. It is a really hard thing to wait out such a serious possibility. It sounds like you are getting very good care so far and that is really half the battle. It is hard to say what is or is not CF from the descriptions we all have of our kids. Mine is one of those really tough cases who shows many symptoms, but lab tests are not adding up. That said, we deal with g-tube feedings for failure to thrive, he is on enzymes, he does CPT and is on nebs and antibiotics for infections often, much like your story. So, my two cents is that even when it could be something else or isn't clear cut, the most important thing I have learned in our 7 year struggle is that the care you receive is the most important thing. Lots of people are misdiagnosed with asthma which can also cause a lot of mucus build up. There could potentially be other things that are causing your daughters difficulties but the treatments are also often the same so I am glad you are getting help and people taking you seriously. I think when we as mothers know something is wrong, doctors need to listen!
I know others will offer a lot more help than I can but I wanted to share my welcome and thoughts. I sure hope you find out something good and helpful soon. Are you also having genetics testing done? Perhaps after the sweat test? No test is 100% but it sure helps to know you have done all you can to figure it out. For us, CF is the one disease that has come up over and over again from all the doctors we have gone to. It hasn't gotten any easier in terms of knowing something concrete, but it has brought our level of treatment up and that is the best I can hope for with my own son for now.
Hang in there, I know how hard this is. Take care and let me know what you find out.
 

mom2owen

New member
Hi, Welcome! I am sorry you are here but I am sure you will get some great ideas from the other members. It is a really hard thing to wait out such a serious possibility. It sounds like you are getting very good care so far and that is really half the battle. It is hard to say what is or is not CF from the descriptions we all have of our kids. Mine is one of those really tough cases who shows many symptoms, but lab tests are not adding up. That said, we deal with g-tube feedings for failure to thrive, he is on enzymes, he does CPT and is on nebs and antibiotics for infections often, much like your story. So, my two cents is that even when it could be something else or isn't clear cut, the most important thing I have learned in our 7 year struggle is that the care you receive is the most important thing. Lots of people are misdiagnosed with asthma which can also cause a lot of mucus build up. There could potentially be other things that are causing your daughters difficulties but the treatments are also often the same so I am glad you are getting help and people taking you seriously. I think when we as mothers know something is wrong, doctors need to listen!
<br />I know others will offer a lot more help than I can but I wanted to share my welcome and thoughts. I sure hope you find out something good and helpful soon. Are you also having genetics testing done? Perhaps after the sweat test? No test is 100% but it sure helps to know you have done all you can to figure it out. For us, CF is the one disease that has come up over and over again from all the doctors we have gone to. It hasn't gotten any easier in terms of knowing something concrete, but it has brought our level of treatment up and that is the best I can hope for with my own son for now.
<br />Hang in there, I know how hard this is. Take care and let me know what you find out.
 
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