Just wondeing...........

julie

New member
<div class="FTQUOTE"><begin quote>That's what I am trying to explain to m husband. He is trying to tell me that even without us being carriers Alayna could still be a carrier but not have it. I know how all of this works but he must be confused. This all came up because we are trying to make our xtended family knowledgeble. </end quote></div>

So, If I read this right he's trying to say that Alayna can be a carrier of a GENETIC mutation that neither of you carry. Unless mutations are starting to spontaneously create themselves in people, that isn't at all possible. However... he might have read some stories about ONLY one parent being a carrier of a mutaiton and a child still ending up with CF. This is possible and it's called uniparental disomy, very rare, but possible. It's when the same mutaiton is inherited twice from the same parent. Similar to how downs occurs in utero with the deletion of one chromosome. For some reason, the chromosome (which happens to be carrying the CF mutation- chromosome 7 in the situaition we are talking about) duplicates itself inside the embryo, so the baby will get 2 of the same chromosomes from one parent, when all the other chromosomes are 1 from mom and 1 from dad.

View this link: <a target=_blank class=ftalternatingbarlinklarge href="http://forums.cysticfibrosis.com/messageview.cfm?catid=5&threadid=9544&highlight_key=y">http://forums.cysticfibrosis.c...d=9544&highlight_key=y</a> 4th post up from the bottom is a post from Steven Keiles, director of genetic services at Ambry genetics. His post might help your husband understand a bit better (also, reading the initial post and subsequent posts might also help.

<div class="FTQUOTE"><begin quote>its not that big of a deal about family members getting tested but i guess when its such a shock when you have no knowledge of this disease that you'd just like to know how many other family members are carring the same gene and try and find out which side of the family it originated from jsut a little bit of medical history just like any other disease that can be passed on. I know the chances of the children being born with CF is 1 and 4 and like with any pregnancy it is a chance you take to have a healthy baby these children are precious angels but to know a lilttle about the disease and the history of it would have been nice instead of during the middle of an ulstrasound and you are 5 months pregnant and they tell you we something wrong and its something that you know nothing about and the genetic counselors make it sound like a death sentence (or at least the one we dealt with). I guess trying to get family members to get tested is not that important but just medical history that can be used for further generations. </end quote></div>

Not sure if the above quoted post is from you Jennifer, because the post was anon. but if it was, just wanted to help clairify one more thing. Just because you, and your husband are carriers, does NOT mean that any of your siblings are carriers. Provided that either your mother or father is a carrier (which at LEAST one of them has to be since you are a carrier, it's possible also for both of them to be carriers) and provided that either your husbands mother or father is a carrier (which at LEAST one of them has to be since he is a carrier, it's possible also for both of them to be carriers), your siblings (for both you and your husband) had a 50% chance of being a carrier (which both of you are) and a 50% chance of not being a carrier. these percentages change if BOTH of your parents were carriers. This page on my website might help illustrate it for your husband also: <a target=_blank class=ftalternatingbarlinklarge href="http://www.cysticfibrosismaleinfertility.com/Where_to_begin_carrierTesting.html">http://www.cysticfibrosismalei...in_carrierTesting.html</a> Look specifically at A. for your daughters CF, and look at D. for yourself and your husband (again, provided that ONLY one of each of your parents are carriers, if both of them are carriers, then you would look at A. again.

I see from your post that you know/understand this, but I thought maybe reinterating it might help your husband understand if he were to come here and read the posts. If you are trying to talk to your family about it and they are in denial (like many families are, "there's no family history, it won't happen to us, it must be 100% from your spouses side") then there's only so much you can do to try and educate them before just considering it a lost cause. Some people, at all costs, will deny that anything like this came from "their side of the family" (gasp!!).

My husbands family has NO history of CF or anything that anyone could recall... until they pulled out the old family records stored in a safe somewhere. Turns out a few generations ago (we are talking like 100 years++), there were some young men (and back then, the men were heavily documented, but not so much the women) died at a young age of complications with lungs and malnutrition. Knowing what we know now, it's pretty safe to assume that these men died from CF. But unless we had pulled out those family records, nobody would have known. Also, if nobody had kept family records we never would have known either. And not every family keeps extensive, or even keeps family records.

Hope this helps a bit, it took me quite a long time to understand it all so maybe your husband is just trying to get a logical grip on all of it. Bottom line, his thinking about how this RECESSIVE CF gene is passed, is wholly incorrect. But, maybe directing him to some of these posts might help him figure it out. Good luck!!
 

anonymous

New member
you've got that right they seems to think that its just going to be on our family only which could very well be as long as their kids or grandkids (if they are carriers as well) don't happen to run into someone who is also a carrier they won't even find out if the gene is going through their immediate families some of the family members already have grandkids and soon to be great grandkids but like you said its a fluke for our family and won't happen to them and I hope it doesn't but I just feel medical history is important but thats on them if they want to find out about it jsut for future reference . I guess i would just like to know even if I weren't personally affected if it were a different family member I would still have gone through the testing jsut to know what the chances are in my family for future generations.
 

ejwiegert

New member
<div class="FTQUOTE"><begin quote>In our situation, I believe that DH and I shouldn't take the 1/4 chance knowing what we know now. Knowing several people who have more than one child wcf. But that's us. And several other factors -- we're over 40 and had planned to have two kids before we got to this age, and things just changed.</end quote></div>

Liza,

Dave and I felt the same way even though we had originally wanted 3-4 children. After Abby was dx'ed in utero and we had Lucy tested and discovered she was a carrier, we decided pretty quickly we didn't want to play "roulette" with a child's life. It was one thing not knowing, but for us, it is a completely different way of thinking now that we know that there is that 1/4 chance. We might not get as lucky as we did with Abby the next time. I just couldn't do that to a child. It was a surprisingly easy decision to make and we had me "fixed" when we went in for Abby's delivery this past Monday.

Interesting post, originator...js7881.

Emily
 

anonymous

New member
When DS was diagnosed, my MIL thought that she and my FIL should be tested, see who was the carrier. IMO thought it was kinda silly. Was she trying to figure out who to blame? What's done is done and we KNOW that DH and I are carriers. His brother and my sis and brother are done having kids, as have most of our first cousins. Luck of the draw -- we're the only family members who have a child wcf. Liza aka ratatosk
 

anonymous

New member
Hi I am Jennifers mom(js7881) the originator of this posting and thank you guys that have answered to this post it has made me see that we are not alone in this situation of other family members I guess they just figure it won't happen to them and it may not but in years to come it could show up again in someone besides Alayna we have had some further testing on myself, Jennifers dad, and brother and it found that her dad passed the gene to both her and her brother so in years to come and he decides to start his family at least we know that he carries the gene also. I guess it was just a curiosity thing on my part to know which of us passed it on to them. But as far as everyone else they see no need in being tested if just the brothers and sisters were to be tested then they would know if any nieces or nephews needed to be tested. If they aren't carrying the gene then their kids wouldn't either and that would be the end of all testing my husband is from a family of 9 he's the youngest he may be the only carrier and then he may not be and from what i see we'll never know unless someone else comes across and unfortunately ends up with it. He is hispanic also which is quite uncommon from what I have read.

And Julie thank you. You seem so knowledgable about this disease and thanks for clearing up the debate on the genetics for Alayna
 

julie

New member
I can completely understand that. I'm the type of person who is curious to the death about things <img src="i/expressions/face-icon-small-smile.gif" border="0">. It's not a matter of who's to blame or whatever, it's just pure curiosity about WHERE/WHO the mutation came from. No harm in figuring that out.

You sure aren't alone (as you stated) about other family members being in denial. In our family, the only person to get tested was Mark's brother, and he's not even a carrier, so each of them got one extereme or the other. His mom's sisters didn't think testing was necessary for them (not because the'd deal if it happened to them, but becaus they thought it WOULDN'T happen to them), and luckly, none of their kids have CF, but they could be carriers (I guess we'll never know), and that just keeps getting passed on and passed on. His cousins have kids now and their kids could be carriers, what happens when those kids marry another carrier... CF all over again. It would be nice if people would just educate themselves a bit. But you'll find as you go through life with Jennifer and Alyana, that many people won't educate themselves and are very ignorant. Just try not to take it too personally (it's hard to do sometimes).

Hope you got all the questions answered!!!! Best of luck with your family, maybe in time they will come around. CF is being discussed publicly more than it ever has before, who knows, maybe in time.....
 

anonymous

New member
Well, this may not be a very popular thought here but when my child with CF was diagnosed, we were told DF508+UNKNOWN mutation. So we tested through Quest, they (Quest) came up with a very uncommon mutation (only one other person in the registry with it). They (Quest) suggested that we (parents) both have genetic screening done to find out <b>IF</b> one of us actually carries the rare mutation or if it was a "spontanious" mutation in our child. We did not do that because we are done having children no matter what so we didn't feel the need. However, it does put a kink in the common thought that the mutations <b>HAVE</b> to be passed down from the parents...we all know strange things happen and genetics are certainly no exception.

Okay, back to the previously scheduled program!
 

amber682

New member
My hubby asked me about that once. For example, can someone be a carrier because the gene mutated to some unknown mutation, not because they inherited a mutated gene? Although I'm sure the chances of that are tiny. But wouldn't that be how the first person to have the mutated gene got it? Feel free to correct me if I'm wrong, I'm just curious.
 

mtmonroe

New member
My daughter DOES not have CF. My husband is a carrier and I have CF. the docs told us we had 1 out of 2 chances of a child with cf. I have 2 older brothers one is a carrier and the other one is not.
 

anonymous

New member
<div class="FTQUOTE"><begin quote>Unless mutations are starting to spontaneously create themselves in people, that isn't at all possible. </end quote></div>

Aren't genetic mutations just a gene that has mutated (which would mean that when each mutation was first created, it was spontaneous since no one "programs" our genes)?? I mean yes, a genetic mutation can be passed on but why would we think that all of the thousand + CF mutations have been around since the human race began?

This is how it was explained to me by a genetics counselor - using layman terms so I could understand it, lol...

A mutation on the CFTR protein is not something that has been added to the protein but rather like a scratch in the protein that damages it and causes malfunction. The names of the mutations tell us where on the protein the "scratch" is located (for example the most common location for a "scratch" is at DF508). These "scratches" can be passed on but they can also just happen out of nowhere (very rare but does happen).

Genetics are very complicated and I am not implying that I know everything or even very much about them - just thinking outloud I suppose!
 

amber682

New member
To above anonymous: You worded it much better than me, but that's what I was getting at.<img src="i/expressions/face-icon-small-smile.gif" border="0">
 
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